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Anti-Trifunctional enzyme subunit beta, mitochondrial, FITC

Anti-Trifunctional enzyme subunit beta, mitochondrial, FITC

Item no.	ARP-15-1230-3
Manufacturer	American Research Products
Amount	100 ul
Category	Antibodies Primary Antibodies
Type	Antibody Polyclonal
Applications	WB, ELISA
Specific against	Human (Homo sapiens)
Host	Rabbit
Isotype	IgG
ECLASS 10.1	32160702
ECLASS 11.0	32160702
UNSPSC	12352203
Available
Description	Defects in HADHB are a cause of trifunctional protein deficiency (TFP deficiency) [MIM:609015]. The clinical manifestations are very variable and include hypoglycemia, cardiomyopathy and sudden death. Phenotypes with mainly hepatic and neuromyopathic involvement can also be distinguished. Biochemically, TFP deficiency is defined by the loss of all three enzyme activities of the TFP complex.
Immunogen	Recombinant human Trifunctional enzyme subunit beta, mitochondrial protein
Form	FITC Conjugated in PBS
Storage	Store at 2-8C for immediate use or -20C for long term storage, avoid repeat freeze thaws.

Note: The presented information and documents (Manual, Product Datasheet, Safety Datasheet and Certificate of Analysis) correspond to our latest update and should serve for orientational purpose only. We do not guarantee the topicality. We would kindly ask you to make a request for specific requirements, if necessary.

All products are intended for research use only (RUO). Not for human, veterinary or therapeutic use.

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Amount: 100 ul

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Delivery expected until 9/18/2025

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